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Wherever this "skin band" grows, the limb will shrink and eventually face amputation
Author丨Huang Wanfeng
Before he was born, he already had 3 toes "strangled" by "skin bands".
After birth, he also had 12 "leather bands" on his body, all over his limbs.
To avoid amputation, he was pushed into the operating room at just two months old, becoming the youngest surgical patient in Yiwu Central Hospital.
On June 16, an eight-and-a-half-pound baby boy fell to the ground. When Mr. Wang embraced his son with the excitement of becoming a father for the first time, he was stunned by what he saw - his son Chengcheng (pseudonym) not only had 3 toes "congenital amputation", only half of them remained, and his limbs were strangled out as if they were tied with "leather bands".
Obstetricians say that wherever this "skin band" grows, the limbs will atrophy and eventually face amputation, which is very scary! What kind of rare disease is this, so terrible?
The answer is in the web version of the doctor's website, identify the QR code below, you can clearly diagnose the child!
"This disease, the provincial doctors have never seen it?!" Just a few days after his birth, he embarked on a tortuous road to seek medical treatment
The doctor's words made Mr. Wang's family panic, and they immediately rushed to Hangzhou with Chengcheng to consult everywhere for medical treatment. Recalling the situation, Mr. Wang said: "My son has not yet come out of the full moon, and there are already several large provincial hospitals, and some hospital doctors do not know this problem. Finally, a doctor at a hospital said: No problem, let's go back to the hospital. ”
After returning to Yiwu with a nervous mood, Chengcheng's grandfather found that the color of Chengcheng's feet was getting purple and purple! Through the introduction of a doctor friend, Mr. Wang contacted Professor Fang Yousheng of Shanghai Huashan Hospital, an authority on hand and foot deformities in China. Professor Fang suggested that he immediately contact Zhou Yang, deputy chief physician of the Department of Hand and Foot Surgery of Yiwu Central Hospital, to arrange the operation as soon as possible. Mr. Wang couldn't help but break into a cold sweat: "Fortunately, we contacted Professor Fang in time, and later we learned that there are no more than 10 hospitals in the country that carry out surgery on this disease, and Professor Fang is an authority in this field in China and has the most experience in surgery." ”
"At such a young age, how risky is the operation?" The doctor encountered two problems
From the first time he saw Chengcheng, a dilemma was placed in front of Zhou Yang.
"The first time the child came, it was not yet a full moon. During the fetal period, 3 toes of the right foot were cut off and could not be recovered. Now there are as many as 12 limbs, the left hand and the left foot are the most, the most serious of which is located in the left calf.
The cause of this disease is inconclusive, there is no reliable preventive measures, only early detection and early treatment, once diagnosed, it is necessary to release the "skin band" of the entrapment as soon as possible, restore the blood supply of the limb, in order to avoid further necrosis of the affected area. Like this situation, if not operated in time, the baby's bones are growing, the muscles are growing, and the band ring not only does not grow, but is constantly contracting, the tighter the clamp, will cause ischemia, necrosis, atrophy of the distal tissue at the stuck site, then it is too late to do surgery, can only amputate. ”
But for such a small baby, surgery is also very risky.
"Patients over a hundred years old have had surgery, and our hospital has had it. The two-month-old baby had surgery that we had never done before. Zhou Yang said, "This operation requires general anesthesia. The baby's development is immature in all aspects, the cardiopulmonary function is not perfect, the anesthesia is very difficult, and the surgical risk is also large. Therefore, if the congenital disease requires surgery, it is recommended to do it after 6 months. ”
Severe entrapment symptoms are called the "emergency" of congenital diseases, and surgical treatment is a race against time!
After a comprehensive assessment, Professor Fang and Zhou Yang agreed that after two months of completion, the most severe left calf would be operated on first to avoid deterioration. After half a year of age, the adult is more mature and undergoes multi-site surgery. If it goes well, after a total of three surgeries, Chengcheng is expected to return to normal by the first birthday.
"He is the youngest surgical patient in our hospital," and the vascular nerves were pressed as thin as pieces of paper
The operation was scheduled for August 16, the day two months were completed. Professor Fang Yousheng rushed to Yiwu Central Hospital to personally lead the surgery, and Dr. Zhou Yang served as an assistant.
At 2 p.m., the first surgery started on time.
"After cutting the subcutaneous tissue, it was found that the soft tissues such as the fat layer and muscle of the child had been jammed and did not connect up and down. The blood vessels have been jammed as thin as pieces of paper, and the nerves have been flattened. ”
Zhou Yang said, "Fortunately, the operation was carried out in time, otherwise it would not be long before the blood vessels would be embolized and lose their effect." The consequences are unimaginable. ”
After more than an hour of surgery, the "skin band" was removed, the nerve and blood vessel function returned to normal on the spot, and the faults of the muscle and fat layers were reconnected, and the operation was successful.
Another highlight of this operation is that the flaps of the previous surgical incisions were all cross-sutured, which Professor Fang improved in a large number of practices, using circular incisions and straight sutures, which not only increased the speed of surgery, but also had less trauma and small scars, which were almost invisible when they grew up. The healing effect is equally good, with no sequelae.
Is it easy to be mistaken for skin streaks? Scientific discernment has a knack
The disease cannot be prevented at present, and prenatal mainly relies on B-ultrasound and MRI. Postpartum can be visually recognized, but can easily be misdiagnosed as striae produced by infant obesity. So how to quickly discern? The doctor reminds everyone that the skin lines are easy to stretch, and the disease shows deep entrapment, local hardness, and cannot be stretched. In severe cases, edema may occur, and the distal limb will have a change in skin color.
If a similar situation is found, it is necessary to immediately seek medical treatment in a hospital that has the ability to diagnose and treat the disease.
Source: Medical Community Responsible Editor: Huang Lan
* The "Medical Community" strives to publish content that is professional and reliable, but does not make any commitment to the accuracy of the content; Relevant parties are requested to check separately when adopting or using it as a basis for decision-making.
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