There is a group of children in this world, they are neither big stomachs, nor foodies, nor "foodies", but they have an almost crazy obsession with food, and whatever they think they can eat will go into their stomachs - whether it is in the trash, pets, or even pills, they will eat.
From birth, they never feel full!
They have a common name called Little Fat Willi Syndrome Sufferer.
1. What is Little Fat Willy syndrome?
Little Fat Willi syndrome, also known as Prader-Willi syndrome (PWS), is a congenital disorder with an incidence of about 1 in 15,000. The main cause is a defect in the function of a gene in the paternal chromosome. This rare disease is also one of the most common genetic causes of severe obesity in children.
One of its most important manifestations is "no satiety". In addition, patients usually have low metabolism, which can easily cause rapid weight growth and become "fat". If they can't control their mouths, they will even face the end of "supporting death" and "fat death".
Because of irresistible appetite and food asking behavior, they will be severely obese, which in turn will lead to a series of complications, such as metabolic disorders, high blood pressure, sleep apnea, etc., and even sudden death.
A 12-year-old girl in Hangzhou, because of Little Fat Willy syndrome, weighed nearly 100 kilograms, entered the ICU three times, in addition to lung infections, respiratory failure, diabetes, high blood pressure and so on.
You might ask why they don't lose weight? That's the experience of the "little fat guys" that you didn't know.
Because the hypothalamus is dysfunctional, they can show an irresistible appetite and strong demanding. Weight loss, something that is sometimes difficult for normal people to do, for them, it will only be harder.
Especially around the age of 8, they begin to show the characteristics of "not being full", losing their temper because they can't eat, and even stealing, "harder than raising 10 children."
At present, there is no specific drug that can cure this gene defect disease, but if it can be found within 1 year of age, growth hormone can be given to improve, reduce their future obesity risk, increase growth rate, reduce fat accumulation, and enhance exercise and language level.
Therefore, early detection is the most critical factor in controlling this disease.
Second, how does Little Fat Willy syndrome manifest
Because it is a congenital disease, children with Little Fat Willi syndrome will have some manifestations of diseases from birth, such as:
(1) Neonatal period and early infancy: low muscle tone, poor sucking ability, feeding difficulties, and even slow or stagnant development;
(2) Late infancy and early childhood: began to overeat because they could not feel "full", and gradually developed into morbid obesity, backward cognitive and language ability;
(3) Adolescence: obvious behavioral problems, resulting in centripetal obesity and related complications due to uncontrolled diet and low metabolic rate; Concurrent delayed puberty, often accompanied by hypogonadism;
(4) Adulthood: short stature, quality of life and survival depend on the degree of obesity, related complications, and mental state.
In addition, they often have difficulty keeping up with their peers in other abilities, with varying degrees of cognitive impairment, motor and language backwardness; The personality is usually irritable, stubborn, compulsive, etc., and has problems such as short stature, facial deformity, scoliosis, etc.
Even more tearful is their appetite that can never be satisfied.
There is a little fat Willy syndrome child named Yangyang in the variety show "Shining Pediatrician", who almost starved to death due to muscle weakness when he was born unable to suck, and when he grew up, because he couldn't perceive "fullness", he would stuff anything he saw into his mouth - and the trash can was no exception.
They can only rely on parental control and the self-control that their parents have worked hard to cultivate to barely control themselves. But the personality traits of "anger, stubbornness, and confrontation" make it difficult for "little fat people" to really diet.
Yangyang's father is very afraid that the child will end up with a "fat death" (death of heart failure due to excessive obesity) like the Internet celebrity "Little Fat" Xu Zhoulei, so he resigned to help Yangyang lose weight. Yangyang was also once the "best little fat little fat body" in the department.
3. What can I do when I encounter such children in daily life?
Like "Moon Child", "Porcelain Doll" and "Butterfly Baby", "Angel Who Can't Eat" cannot be cured, but can only be controlled by strict diet and behavior control, and growth hormone.
In foreign countries, "Little Fat Willy" has been classified as severely disabled and needs to be supervised; In China, the disease was also included in the "First Rare Disease List" in 2018.
If we encounter "little fat", please be gentle with them, and when they "crazy rice", be tough and help them control. You know, for them, gluttony is not a mistake, they are just sick.
Don't cast a strange look at them: it's hard to get caught up in an appetite vortex than other vibrant children, not to mention the complications of "overload" fat and fatty liver. While physically affected, their mental state is also difficult to maintain stability, and strange vision can only aggravate their paranoia.
Every child is an angel, and angels who don't have enough to eat are angels. I wish every child health, and I wish every "little fat" can receive proper care and intervention.